Unilateral and multiple nodular plexiform Neurofibromas: An uncommon presentation of Neurofibromatosis type 1
نویسندگان
چکیده مقاله:
Plexiform neurofibroma is a rare variant but pathognomonic of von Recklinghausen disease. We report an uncommon presentation of neurofibromatosis type I in a girl. This 11-year old girl had multiple plexiform neurofibromas on her left hand, and also several Lisch’s nodules. Classification and clinical features are discussed briefly with emphasis on the possibility this condition may not be given sufficient consideration.
منابع مشابه
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عنوان ژورنال
دوره 3 شماره 4
صفحات 46- 51
تاریخ انتشار 2000-07-01
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